Chiari malformation

Structural defects in the base of the skull and cerebellum. A congenital neurological condition that can cause neurological problems including balance.

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Tests and scans 548556991.jpg

What is a chiari malformation?

Chiari malformation is a condition where brain tissue extends into the spinal canal. This happens when there is a mismatch between the size of brain tissue and the brain cavity, so the tissue is pushed downwards into the spinal canal. This can put pressure on the brainstem and spinal cord, sometimes resulting in the formation of a cyst within the spine.

Need to know

Many people with a Chiari malformation have no signs or symptoms so the condition often goes unnoticed. However, symptoms can occur depending on type and severity of the Chiari malformation:

Chiari I: Usually becomes apparent in late childhood/early adulthood. Symptoms can include coughing, headaches and balance problems.If associated with a spinal cyst (syringomyelia), it can also cause poor hand coordination, difficulty walking and difficulty swallowing (syringobulbia).

Chiari II: Always related to an open spina bifida. Symptoms can include changes in breathing, swallowing problems, quick downward eye movements and arm weakness.

As Chiari malformations have few symptoms, they are often discovered during physical examinations. They may show up on the following tests:

  • MRI scans to display brain tissue clearly
  • X-rays may reveal bone abnormalities associated with Chiari malformation
  • CT scans can help display bone abnormalities associated with Chiari malformation
If the Chiairi malformation is causing you headaches and pressing on your spinal cord, your consultant may recommend medication or decompression surgery.

Your surgeon will make a cut at the back of your head and then remove a piece of bone removed from the base of your skull. Normally the arch of the first vertebra (C1) is also removed. The bony decompression between the occiput and the C1 vertebra allows the tough outer covering of the brain and spine (dura) to be opened, creating more space for the abnormally-located brain tissue.

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This content is intended for general information only and does not replace the need for personal advice from a qualified health professional.